Search on: FACTOR IX 
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Descriptor English:   Factor IX 
Descriptor Spanish:   Factor IX 
Descriptor Portuguese:   Fator IX 
Synonyms English:   Blood Coagulation Factor IX
Factor IX Complex
Factor IX Fraction
Complex, Factor IX
Factor IX, Coagulation
Fraction, Factor IX
IX Complex, Factor
IX Fraction, Factor
IX, Coagulation Factor
Christmas Factor
Plasma Thromboplastin Component
PTC
Autoprothrombin II
Coagulation Factor IX  
Tree Number:   D12.776.124.125.375
D23.119.375
Definition English:   Storage-stable blood coagulation factor acting in the intrinsic pathway. Its activated form, IXa, forms a complex with factor VIII and calcium on platelet factor 3 to activate factor X to Xa. Deficiency of factor IX results in HEMOPHILIA B (Christmas Disease). 
Entry Combination - descr/qualif English:   Factor IX/deficiency use Hemophilia B
 
See Related English:   Coagulants
 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AN analysis
AI antagonists & inhibitors BI biosynthesis
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects SE secretion
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   22169 
Unique Identifier:   D005164 

Occurrence in VHL:
 

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